| CASE REPORT |
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| Year : 2022 | Volume
: 17
| Issue : 4 | Page : 945-948 |
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Gorlin-goltz syndrome
Pragati Anupkumar Bhargava1, Rahul R Bhowate1, Nikhil Wasudeorao Parate2
1 Department of Oral Medicine and Radiology, Sharad Pawar Dental College, Datta Meghe Institute of Medical Sciences, Deemed to be University, Wardha, Maharashtra, India
2 Mahalakshmi Dental Clinic, Wardha, Maharashtra, India
Correspondence Address:
Dr. Pragati Anupkumar Bhargava
Department of Oral Medicine and Radiology, Sharad Pawar Dental College, Datta Meghe Institute of Medical Sciences, Deemed to be University, Sawangi (M), Wardha, Maharashtra
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/jdmimsu.jdmimsu_477_22
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Gorlin-Goltz syndrome (GGS) is a rare autosomal dominant condition. Diverse incidence rates of this syndrome have been reported all over the world. It is estimated to occur 1 in 50,000–150,000. GGS is of particular interest to dental surgeons and maxillofacial radiologists because of their association with odontogenic keratocysts (OKC). GGS associated with OKCs tend was known to occur in individuals who were at a much younger age. In our case, cysts that were radiographically similar to OKCs were present in our male patient. OKCs associated with GGS are reported to be more frequent in the maxilla than in the mandible. GGS may manifest with the triad of basal cell nevi, keratocysts of the jaws, and deformities in the skeletal system. Recognition of the condition is crucial for establishment for early diagnosis as it can minimize the severity of the condition. The aim of this article was to report a case of GGS who was diagnosed primarily based on craniofacial manifestations.
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